Hemangioendotelioma epitelioide pulmonar. Reporte de un caso
Author
dc.contributor.author
Quiroz, Manuel
Author
dc.contributor.author
Undurraga, Alvaro
Author
dc.contributor.author
Moya, Rafael
Author
dc.contributor.author
Fernández, Cristina
Author
dc.contributor.author
Bezares, Katiuska
Author
dc.contributor.author
Linacre, Virginia
Admission date
dc.date.accessioned
2018-05-23T13:34:50Z
Available date
dc.date.available
2018-05-23T13:34:50Z
Publication date
dc.date.issued
2017
Cita de ítem
dc.identifier.citation
Rev Med Chile 2017; 145: 662-666
es_ES
Identifier
dc.identifier.issn
0717-6163
Identifier
dc.identifier.uri
https://repositorio.uchile.cl/handle/2250/148052
Abstract
dc.description.abstract
Epithelioid hemangioendothelioma is a multifocal tumor that rarely metastasizes. It is difficult to diagnose, most often it is an incidental finding in young asymptomatic women. The radiologic pattern is heterogeneous. Histologic confirmation of Weibel-Palade bodies or immunohistochemistry based on specific tumor markers such as factor VIII and CD34 are the most important finding to confirm the diagnosis. We report a 21 years old woman Presenting with cough and dyspnea. A chest X ray was suggestive of tuberculosis. Sputum smears were negative for acid fat bacilli and the tuberculin test was negative. A chest CAT scan showed multiple nodular lesions. A surgical biopsy of the lesions confirmed the presence of a hemangioendothelioma. The patient was initially treated with prednisone and azathioprine without response. Thereafter, the patient is without treatment and without evidence of disease progression.