IgG4-related disease, the new "great mimicker". Report of one case Enfermedad relacionada a IgG4, el nuevo "gran simulador": Caso clínico
Author
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Erlij Opazo, Daniel
Author
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Ramos, Daniel
Author
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Montaña, Jacqueline
Author
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Kusnir, Paula
Author
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Correa, Gonzalo
Author
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Neira, Oscar
Admission date
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2019-01-29T15:38:30Z
Available date
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2019-01-29T15:38:30Z
Publication date
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2014
Cita de ítem
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Revista Medica de Chile, Volumen 142, Issue 5, 2018, Pages 646-650
Identifier
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07176163
Identifier
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00349887
Identifier
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10.4067/S0034-98872014000500014
Identifier
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https://repositorio.uchile.cl/handle/2250/161927
Abstract
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Due to its multisystem involvement, IgG4 -related disease should be considered in the differential diagnosis of medical conditions such as lymphadenopathies, aortitis, serositis and retroperitoneal fbrosis. It shares features with other entities historically described as "great mimickers" such as syphilis, tuberculosis, sarcoidosis, and systemic lupus erythematosus. We report a 40 year-old male with recurrent effusive - constrictive pericarditis, lymphadenopathy and aortitis. The study revealed an inactive tuberculosis with negative cultures for acid fast bacilli. The patient had high serum levels of IgG4 and a mediastinal lymph node biopsy was consistent with IgG4 -related disease. The patient was treated with prednisone 40 mg/day with an excellent response.