Encefalopatía subaguda en una paciente con policondritis recidivante. Caso clínico
Author
dc.contributor.author
Vera, Constanza
Author
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Matamala Capponi, José Manuel
Author
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Feuerhake Molina, Walter Enrique
Author
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Neira Quiroga, Oscar Javier
Author
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Vidal, Aaron
Author
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Castillo Carrasco, José Luis
Admission date
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2022-05-09T19:40:45Z
Available date
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2022-05-09T19:40:45Z
Publication date
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2021
Cita de ítem
dc.identifier.citation
Rev Med Chile 2021; 149: 1085-1089
es_ES
Identifier
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0034-9887
Identifier
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https://repositorio.uchile.cl/handle/2250/185358
Abstract
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Relapsing polychondritis (RP) is a rare multisystemic autoimmune disorder
characterized by the inflammation and destruction of cartilages, with
preference for auricular, nasal and laryngotracheal cartilages. RP may also
affect proteoglycan-rich structures, such as, blood vessels, eyes, kidneys, and
heart. The central nervous system (CNS) is involved in less than 3% of patients.
We report a 32-year-old female with RP associated with a progressive
subacute encephalopathy characterized by behavioral disturbances, auditory
and visual hallucinations. The EEG showed generalized slow activity and a
mononuclear pleocytosis with increased protein was found in the cerebrospinal
fluid. The brain magnetic resonance imaging showed multiple supra
and infratentorial nodular inflammatory lesions. After initiating treatment
with corticosteroids and cyclophosphamide, a significant improvement in
chondritis and neurological status was observed.
es_ES
Lenguage
dc.language.iso
es
es_ES
Publisher
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Soc. Médica Santiago
es_ES
Type of license
dc.rights
Attribution-NonCommercial-NoDerivs 3.0 United States