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Now showing items 1-10 of 12
ALS-linked protein disulfide isomerase variants cause motor dysfunction
(Wiley-Blackwell, 2016)
Fine-tuning ER stress signal transducers to treat amyotrophic lateral sclerosis
(Frontiers Media SA, 2017)
Creutzfeldt-jakob disease. Report of one case Desafíos en el diagnóstico de enfermedad de Creutzfeldt-Jakob. Caso clínico
(Sociedad Medica de Santiago, 2016)
The ER proteostasis network in ALS: Determining the differential motoneuron vulnerability
(Elsevier Ireland Ltd, 2017)
Disulfide cross-linked multimers of TDP-43 and spinal motoneuron loss in a TDP-43(A315T) ALS/FTD mouse model
(Nature Publishing Group, 2017)
Proteostasis disturbance in amyotrophic lateral sclerosis
(Oxford University Press, 2017)
Functional Role of the Disulfide Isomerase ERp57 in Axonal Regeneration
(Public Library Science, 2015)
Desafíos en el diagnóstico de enfermedad de Creutzfeldt-Jakob. Caso clínico
(Soc Médica Santiago, 2016)